대한신장학회

Skip Navigation: Skip to contents

KOR
ENG
전체메뉴보기

간행물 검색

현재 페이지 경로

HOME
간행물
간행물 검색

논문분류	춘계학술대회 초록집
제목	Fulminant Guillain-Barre' Syndrome And Lupus Nephritis As The Presenting Features In Childhood-Onset Systemic Lupus Erythematosus: A Case Report
저자	Fatima Hannah Romero
출판정보	2024; 2024(1):
키워드
초록	Childhood-onset systemic lupus erythematosus (cSLE) constitutes about 10-20% of all lupus cases. Peripheral nervous system involvement accounts for <10% of cases with neuropsychiatric manifestations. Guillain-Barré syndrome (GBS) as one of the initial manifestations of SLE has rarely been reported in the pediatric age group. Treatment recommendations for GBS in a lupus patient do not exist at present. An 8-year-old Filipjno girl presented with fulminant GBS, lupus nephritis class IV-S(A), myocarditis, and pulmonary hypertension. She received intravenous immunoglobulin (IVIg), methylprednisolone pulses, intravenous cyclophosphamide, and therapeutic plasma exchange (TPE). Favorable treatment response was noted after the 5th TPE and 2nd cycle of IVIg. Adjunct treatment included Digoxin, Aspirin, Enalapril, Propranolol, and Amlodipine. After 4 months from the last plasma exchange, she can talk, move all extremities but still had difficulty ambulating. Due to recurrent infections, Cyclophosphamide was shifted to Mycophenolate Mofetil (MMF) and partial remission was achieved on the 2nd month of MMF. High index of suspicion, timely interdisciplinary care and detailed diagnostic work up needs to be emphasized to overcome the difficulty in managing a rare case despite the lack of specific treatment recommendations.
원문(PDF)	PDF 원문보기

목록

위로가기